Table 1.
Demographics
| Variable | Normal Mitral n=18 | CAVC n=35 |
|---|---|---|
| Age (years) | 3.0 [0.0–4.4] | 0.3 [0.2–0.3] |
| Female gender (n, %) | 9 (50%) | 20 (57%) |
| Height (cm) | 95.0 [51.8–109.1] | 58 [50.9–60.8] |
| Weight (kg) | 14.5 [3.6–18.5] | 4.4 [3.4–5.1] |
| BSA (m 2 ) | 0.62 [0.23–0.75] | 0.27 [0.23–0.29] |
| Heart Rate (bpm) | 99 [83–116] | 136 [126–143] |
| Rastelli Type | ||
| A (n, %) | 20 (57%) | |
| C (n, %) | 15 (43%) | |
| Trisomy 21 (n, %) | 29 (83%) | |
| Pre-repair Qualitative Ventricular Function of Native CAVC | ||
| Normal (n, %) | 100% | 32 (91%) |
| Mildly diminished (n, %) | 2 (6%) | |
| Moderately diminished (n, %) | 1 (3%) | |
| Pre-Repair AVV Regurgitation | ||
| Mild or less (n, %) | 25 (71%) | |
| Moderate or greater (n, %) | 10 (29%) | |
| Post-Repair Right AVV Regurgitation | ||
| Mild or less (n, %) | 28 (80%) | |
| Moderate or greater (n, %) | 6 (17%) | |
| Post-Repair Left AVV Regurgitation* | ||
| Mild or less (n, %) | 21 (60%) | |
| Moderate or greater (n, %) | 13 (37%) | |
| Frame rate (Hz) | 31 [25–37] | 34 [33–43] |
BSA = body surface area; AVV = atrioventricular valve.
Data are expressed as median [interquartile range] or as a number (percentage).
*
only 34 patients underwent CAVC repair