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. 2013 Jun;22(128):163–168. doi: 10.1183/09059180.00001013

Table 3. Summary of evidenced-based treatments for idiopathic pulmonary fibrosis.

ATS/ERS/JRS/ALAT guidelines [2] New evidence 2012
Anticoagulation Weak No Strong No (ACE) [8, 9]
NAC monotherapy Weak No Weak No [2, 11]
Prednisone/azathioprine/NAC Weak No Strong No (PANTHER) [9, 13]
Pirfenidone Weak No Weak Yes [22]
(German guidelines [9])

For definitions of Weak No, Strong No and Weak Yes refer to [2]. ATS: American Thoracic Society; ERS: European Respiratory Society; JRS: Japanese Respiratory Society; ALAT: Latin American Thoracic Association; NAC: N-acetylcysteine; ACE: angiotensin converting enzyme; PANTHER: Prednisone, Azathioprine, and N-Acetylcysteine: A Study That Evaluates Response in Idiopathic Pulmonary Fibrosis.