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. 2010 Dec;19(118):308–313. doi: 10.1183/09059180.00007910

Table 1. Pulmonary arterial hypertension associated with congenital heart disease (CHD).

Type of defect Example
Left-to-right shunts Atrial septal defect
Ventricular septal defect
Atrioventricular defects
Patent ductus arteriosus
Left-sided obstruction Mitral stenosis
Aortic stenosis
Cyanotic CHD (occurring with increased pulmonary blood flow) Common arterial trunk
Transposition of great vessels
Anomalies of pulmonary arteries Tetralogy of Fallot with pulmonary atresia and MAPCAs
Hemitruncus

MAPCA: major aortopulmonary collateral artery. Modified from [8] with permission from the publisher.