Table 1. Pulmonary arterial hypertension associated with congenital heart disease (CHD).
Type of defect | Example |
Left-to-right shunts | Atrial septal defect |
Ventricular septal defect | |
Atrioventricular defects | |
Patent ductus arteriosus | |
Left-sided obstruction | Mitral stenosis |
Aortic stenosis | |
Cyanotic CHD (occurring with increased pulmonary blood flow) | Common arterial trunk |
Transposition of great vessels | |
Anomalies of pulmonary arteries | Tetralogy of Fallot with pulmonary atresia and MAPCAs |
Hemitruncus |
MAPCA: major aortopulmonary collateral artery. Modified from [8] with permission from the publisher.