TABLE 2.
Registry | [Ref.] | Incidence per 106 population | Prevalence per 106 population | |
IPPHS | [17] | IPAH | 1.7 | |
French | [8] | IPAH | 1.0 | 5.9 |
French | [8] | IPAH | 2.4 | 15 (4–29#) |
Scottish | [25] | IPAH | 2.6 | 9 |
Scottish | [25] | IPAH | 7.6 | 26 (52¶) |
REVEAL | [9] | IPAH | 0.9 | |
REVEAL | [9] | IPAH | 2.0 | 10.6 |
UK | [10] | IPAH | 1.1 | 6.6 |
Spanish | [11] | IPAH | 1.2 | 5.6 |
Spanish | [11] | PAH | 3.7 | 16 |
Swedish | [5] | IPAH | 5 | 25 |
Data are presented as annual cases per million population for incidence and prevalence. IPAH: idiopathic pulmonary arterial hypertension; PAH: pulmonary arterial hypertension; REVEAL: Registry to Evaluate Early and Long-Term Pulmonary Arterial Hypertension. #: regional differences; ¶: Scottish hospitalisation registry.