FIGURE 2.

Serial high-resolution computed tomography (HRCT) scans at the lung window from patient 2, who developed several episodes of right pneumothorax that required iterative surgical interventions. a, b) Thin-walled cystic lung pattern (note the presence of a drain for the first episode). c, d) Complex right pneumothorax with bullae in the right lung base. e, f) 18 months after the last thoracic surgery, there were residual thin-walled cystic lesions.