Table 4.

HAE Patients’ characteristics.

Number of HAE patients	40
Sex male/female n (%)	14 (35%)/26 (65%)
Median age (range)	34 (21–70)
Disease characteristics
Family history n (%)	30 (75%)
HAE Type n (%) Type 1 Type 2	35 (88%) 5 (12%)
HAE symptoms Mild to Moderate, n (%) Severe, n (%)	21 (52%) 19 (48%)
Biomarker levels
aC1-INH median (g/L) Type 1 Type 2	0.12 0.4
fC1-INH (%) median	20.6
C4 (g/L) median	0.05

aC1-INH—antigen C1-INH concentration (g/L); reference range: 0.21–0.36 (g/L), fC1-INH—functional activity of C1-INH (%); reference range: 70–130%, C4—antigen C4 concentration (g/L); reference range 0.1–0.38 (g/L).