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. 2022 Sep 12;23(18):10573. doi: 10.3390/ijms231810573
AD Alzheimer’s disease
ATP adenosine triphosphate
CoQ10 coenzyme Q10
CNS central nervous system
ERT enzyme replacement therapy
GSH glutathione
LSD lysosomal storage disorders
PD Parkinson’s disease
MPS mucopolysaccharidosis
MRC mitochondrial respiratory chain
NAC N-acetylcysteine
NCL neuronal ceroid lipofuscinoses
NPC Niemann–Pick disease, type C
OXPHOS- Oxidative phosphorylation
PLP pyridoxal phosphate
PNS peripheral nervous system
ROS reactive oxygen species
TNF α-tumour necrosis factor alpha