Table 3.

Schnelldorfer Classification for Polycystic Liver Disease

	Symptoms	Cyst	Areas of Relative Normal Liver Parenchyma	Isosectoral Portal Vein or Hepatic Vein Occlusion of Preserved Sector	Proposed Treatment
Type A	Absent or mild	Any	Any	Any	Observation or Medical treatment
Type B	Moderate or severe	Limited number of large cysts	≥ 2 sectors	Absent	Cyst fenestration
Type C	Severe (or moderate)	Any	≥ 1 sector	Absent	Partial hepatectomy with remnant cyst fenestration
Type D	Severe (or moderate)	Any	< 1 sector	Present	Liver transplantation

Note: Data from Schnelldorfer T et al.184