TABLE 1.

Clinical presentation: in a developmentally normal child, who presents with seizures of unknown cause (normal magnetic resonance imaging, normal laboratory studies, ± normal cerebrospinal fluid studies), genetic testing to exclude DS should be performed with the following seizure types

Seizure	Age 2–5 months			Age 6–15 months
	Without fever	With fever	After vaccination	Without fever	With fever	After vaccination
Single seizure
Prolonged (5–29 min) GTCS	63% a	74% b	74% b	63% a	58% a	68% b
Prolonged (5–29 min) hemiclonic seizure	68% b	84% c	95% c	68% b	84% c	89% c
Focal or generalized convulsive status epilepticus (≥30 min)	74% b	84% c	89% c	74% b	84% c	89% c
Recurrent seizures
Recurrent brief (<5 min) convulsive seizures	63% a	58% a		58% a	58% a
Recurrent brief (<5 min) hemiclonic seizures	68% b	74% b		79% b	79% b
Recurrent prolonged focal or generalized convulsive seizures (5–29 min)	89% c	100% c		84% c	95% c
Recurrent focal or generalized convulsive status epilepticus (≥30 min)	89% c	95% c		89% c	95% c

Based on 19 physician responses.

Abbreviations: DS, Dravet syndrome; GTCS, generalized tonic–clonic seizure.

^a Responses indicate no consensus for genetic testing for DS.

^b Responses indicate Moderate consensus for genetic testing for DS.

^c Responses indicate Strong consensus for genetic testing for DS.