TABLE 3.
Frequency of abnormal values and TE (%) in MUL patients
| ALT | AST | GGT | Bilirubin | Bile acids | Albumin | Prealbumin | TT | FV | Gal½ | APRI | TE | |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| Age | ||||||||||||
| 0–10 | 2/8 (25) | 3/8 (38) | 2/8 (25) | −/8 | 3/7 (43) | −/8 | 1/7 (14) | −/8 | −/7 | −/5 | 2/7 (29) | 3/9 (33) |
| 11–20 | 4/11 (36) | 1/10 (10) | 3/11 (27) | 2/10 (20) | 1/11 (9) | −/12 | 1/10 (10) | 1/11 (9) | −/11 | −/11 | 1/10 (10) | 5/10 (50) |
| >20 | 4/12 (33) | 1/8 (13) | 1/8 (13) | 1/8 (13) | 2/7 (29) | −/10 | 2/7 (29) | −/9 | 1/8 (13) | −/8 | 1/8 (13) | 6/10 (60) |
| Echocardiography | ||||||||||||
| Restriction a | 5/17 (29) | 3/16 (19) | 4/16 (25) | 2/15 (13) | 4/15 (27) | 1/17 (6) | 3/14 (21) | 2/16 (13) | −/14 | −/14 | 2/16 (13) | 8/16 (50) |
| No restriction | 3/8 (38) | 1/6 (17) | 1/7 (14) | −/7 | 1/7 (14) | −/9 | 0/7 | −/7 | −/7 | −/6 | 1/5 (20) | 3/9 (33) |
| ProBNP | ||||||||||||
| Elevated | 4/12 (33) | 2/9 (22) | 3/9 (33) | 1/9 (11) | 3/8 (34) | −/9 | 3/8 (34) | 1/9 (11) | −/7 | −/8 | 2/9 (22) | 5/10 (50) |
| Normal b | 4/14 (29) | 2/13 (15) | 2/14 (14) | 1/13 (8) | 2/13 (15) | 1/15 (7) | −/12 | 1/14 (7) | −/14 | −/12 | 1/12 (8) | 5/11 (45) |
| TE | ||||||||||||
| ≥7 kPa | 4/13 (31) | 2/11 (18) | 4/11 (36) | 3/11 (27) | 3/10 (30) | 1/12 (8) | 2/11 (18) | 4/12 (33) | 1/12 (8) | −/10 | 3/10 (30) | 14/14 |
| <7 kPa | 2/12 (17) | 2/12 (17) | 1/12 (8) | −/11 | 3/12 (25) | −/12 | 2/10 (20) | −/12 | −/10 | −/10 | −/12 | −/15 |
a
Signs of restrictive physiology in echocardiography.
b
Children and adolescents >178, adult males >50, adult females >180.