Table 1.

Diagnostic criteria for triglyceride deposit cardiomyovasculopathy (2020)

Criteria	Clinical findings
Essential	Impaired LCFA metabolism or TG deposition in myocardium
	1. Decreased washout rate (< 10%) in myocardial 123I-BMIPP SPECT
	2. Myocardial TG deposition by biopsy specimens
	3. Myocardial TG deposition by CT or MR spectroscopy
Major	1. Decreased left ventricular ejection fraction < 40%
	2. Diffuse narrowing of coronary arteries documented by CAG and/or coronary CT angiography
	3. Typical Jordans anomaly (apparent vacuoles > 1 μm in size) of polymorphonuclear leucocytes in peripheral blood smears
Supportive	1. Diabetes mellitus
	2. Hemodialysis

Diagnosis Definite TGCV: Meets one or more essential criteria and one or more major criteria

Probable TGCV: Meets at least one essential criterion

¹²³I-BMIPP, ¹²³I-β-methyl iodophenyl-pentadecanoic acid; CAG coronary angiography, CT computed tomography, LCFA long chain fatty acid, MR magnetic resonance, SPECT single-photon emission computed tomography, TG triglyceride, TGCV triglyceride deposit cardiomyovasculopathy