Table 1.
Demographic and clinical characteristics of patients with cutaneous sarcoidosis.
Age at diagnosis; years | |
Mean (SD) | 52.2 (12.5) |
Median (range) | 54.0 (22.0–77.0) |
Sex, n (%) | |
Male | 16 (43%) |
Female | 21 (57%) |
Morphology of cutaneous disease, n (%) * | |
Specific cutaneous sarcoidosis | |
Papules | 16 (43%) |
Plaques and nodules | 9 (24%) |
Subcutaneous (Darier-Roussy disease) | 1 (3%) |
Scar-associated | 1 (3%) |
Non-specific cutaneous sarcoidosis | |
Erythema nodosum | 10 (27%) |
Localized involvement, n (%) | 14 (38%) |
Systemic involvement, n (%) | 23 (62%) |
Bilateral hilar lymphadenopathy | 23 (62%) |
-Severe hilar lymphadenopathy (≥stage II) | 6 (16%) |
-Impaired lung function | 11 (30%) |
Arthritis | 11 (30%) |
Splenomegaly | 6 (16%) |
Uveitis | 2 (5%) |
Neurosarcoidosis | 1 (3%) |
Lofgren syndrome | 4 (11%) |
Disease course, n (%) | |
Chronic | 26 (70%) |
Acute | 11 (30%) |
Management, n (%) | |
Topical corticosteroids | 24 (65%) |
Systemic corticosteroids | 12 (32%) |
NSAID | 5 (13%) |
Hydroxychloroquine | 2 (5%) |
Methotrexate | 1 (3%) |
Azathioprine | 1 (3%) |
Doxycycline | 1 (3%) |
Infliximab | 1 (3%) |
n, number; SD, standard deviation; NSAID, non-steroidal anti-inflammatory drugs.