Table 3.

Interventions of SNHL in reported MDPL

Previous publications	Age at SNHL onset (years)	Interventions
Shastry et al. [1], patient 100.3	18	NA
Shastry et al. [1], patient 200.5	15	NA
Shastry et al. [1], patient 300.4	7	NA
Shastry et al.[1], patient 400.3	8	NA
Shastry et al. [1], patient 500.4	16	NA
Shastry et al. [1], patient 600.4	14	NA
Shastry et al. [1], patient 700.3	6	NA
Weedon et al. [2], patient 1	12	Bilateral hearing aids
Weedon et al. [17], patient 2	33	NA
Pelosini et al. [9]	25	Hearing aid
Reinier et al. [10]	10	NA
Lessel et al. [3], patient 1	N	NA
Lessel et al. [3], patient 2	12	NA
Lessel et al. [3], patient 3	11	NA
Lessel et al. [3], patient 4	N	NA
Lessel et al. [3], patient 5	14	NA
Lessel et al. [3], patient 6	14	NA
Lessel et al. [3], patient 7	N	NA
Lessel et al. [3], patient 8	NA	NA
Ajluni et al. [18], patient 6	N	N
Ajluni et al. [18], patient 7	N	N
Elouej et al. [7], patient 1	N	N
Elouej et al. [7], patient 2	4	Bilateral hearing aids
Okada et al. [11]	7	Hearing aids
Wang et al. [12]	10	Hearing aids
Fiorillo et al. [13]	2	NA
Sasaki et al. [14]	Puberty	NA
Wang et al. [15]	15	NA
Oh et al. [8], SB127-219	NA	NA
Oh et al. [8], SB127-277	NA	NA
Yu et al. [16]	25	NA
Zhou et al. [17]	20	NA
Murdocca et al. [6]	NA	NA
This study proband	6	Bilateral hearing aids

SNHL, sensorineural hearing loss; MDPL, mandibular hypoplasia, deafness, progeroid features, and lipodystrophy syndrome; N, no; NA, not available