6MWD	6 min walk distance
AV	Arterio-venous
BMI	Body Mass Index
BMPR	Bone morphogenic protein receptor
cAMP	Cyclic adenosine monophosphate
CCB	Calcium channel blockers
cGMP	Cyclic guanosine monophosphate
CI	Cardiac index
CO	Cardiac output
COPD	Chronic obstructive pulmonary disease
COX	Cyclo-oxygenase
Cpc	Combined post and precapillary
CTD	Connective tissue diseases
CTEPH	Chronic thromboembolic pulmonary hypertension
DCA	Dichloroacetate
DOACS	Direct oral anticoagulants
ERA	Endothelin receptor antagonist
ET	Endothelin
FC	Functional class
FDA	Food and Drug Association
GD	Gaucher disease
HFpEF	Heart failure with preserved ejection fracture
HFrEF	Heart failure with reduced ejection fracture
ILD	Interstitial lung disease
IPAH	Idiopathic pulmonary arterial hypertension
Ipc	Isolated postcapillary
JVD	Jugular venous distension
Kv	Potassium gated ion channel
LAP	Left-atrial pressure
LHC	Left-heart catheterization
LHD	Left-heart disease
LV	Left ventricle
LVEDP	Left-ventricular end-diastolic pressure
mPAP	Mean pulmonary artery pressure
NO	Nitric oxide
NT-pro BNP	N-terminal pro-B-type natriuretic peptide
OSA	Obstructive sleep apnea
PA	Pulmonary artery
PCA	Prostacyclin analog/agonist
PCWP	Pulmonary capillary wedge pressure
PDE-5	Phosphodiesterase 5
PDGF	Platelet-derived growth factor
PGI2	Prostaglandin I2
PLCH	Pulmonary Langerhans cell histiocytosis
PTE	Pulmonary thromboendoarterectomy
PVR	Pulmonary vascular resistance
RCT	Randomized control trial
RV	Right ventricle
SAPH	Sarcoidosis-associated PH
SCD	Scleroderma
SQ	Subcutaneous
TGF-B	Transforming growth factor-beta
TTCW	Time to clinical worsening
TTE	Transthoracic echocardiography
V/Q	Ventilation and perfusion
WHO	World Health Organization