Table 2.
Epidemiological data of the Hannover cohort
| Dystonia form | Age [years/mean±SD] |
Sex ratio [m:f] |
Frequency [% of all dystonia patients] |
Prevalence [n/1mio] |
Extrapolated prevalence in Germany [n] |
|---|---|---|---|---|---|
| Cervical dystonia | 63.8 ± 13.9 | 0.3 | 42 | 251.1 | 20,387 |
| Blepharospasm | 69.4 ± 12.5 | 0.4 | 15 | 87.5 | 7105 |
| Writer's cramp | 62.0 ± 16.6 | 0.5 | 9 | 55.2 | 4479 |
| Tardive dystonia | 67.0 ± 19.7 | 0.3 | 6 | 38.0 | 3089 |
| Musician's dystonia | 50.2 ± 14.4 | 1.8 | 5a | 32.3a | 2626a |
| Psychogenic dyst | 47.2 ± 20.8 | 1.1 | 5 | 28.5 | 2317 |
| Generalised dystonia | 51.7 ± 14.8 | 0.3 | 4 | 26.6 | 2162 |
| Spasmodic dysphonia | 60.4 ± 17.5 | 0.4 | 3 | 24.7 | 2008 |
| Segmental dystonia | 62.6 ± 13.5 | 0.2 | 3 | 20.9 | 1699 |
| Arm dystonia | 70.5 ± 12.5 | 0.6 | 3 | 15.2 | 1236 |
| Oromandibular dyst | 46.7 ± 15.8 | 0.8 | 2 | 13.3 | 1081 |
| Leg dystonia | 1 | ||||
| Hemidystonia | 0 | ||||
| Total | 62.4 ± 16.1 | 0.4 | 100 | 601.1 | 48,806 |
aExplanation in Discussion