Feature | MHC Class II Deficiency (n = 8) Median (range) or N |
CGD (n = 8) Median(range) or N |
---|---|---|
Age (years) | 1.71 (0.5-5.1) | 7.14 (5.1-11) |
Gender (F/M) | 4/4 | 2/6 |
MRD/MUD | 7/1 | 7/1 |
Cumulative Busulfan level (mg/L.h) | 57 (50-70) | 52.7 (46-62) |
Time to Neutrophil engraftment (days) | 24(16-30) | 20 (17-26) |
Time to Platelet engraftment (days) | 33(25-65) | 18(17-47) |
Infused nucleated cell dose (X 108/kg) | 5.7 (4-14) | 4.2 (1.1-7.5) |
Infused CD34 cell dose (X 106/kg) | 12 (2.51-21.9) | 7.6 (3.3-10.7) |
Acute GVHD Grade II-IV | 1 (grade II) | 1 (grade II) |