Table 1.

Clinical characterization of IEI patients with lymphoma

	CVID	APDS	DNA repair deficiency	P value CVID vs APDS	P value CVID vs DNA repair deficiency	P value APDS vs DNA repair deficiency
No. of patients	14	4	5
Sex				0.2745†	0.1409†	1.0000†
Male (%)	9 (64%)	1 (25%)	1 (20%)
Female (%)	5 (36%)	3 (75%)	4 (80%)
EBV status				1.0000†	0.1409†	0.5238†
Positive (%)	5 (36%)	2 (50%)	4 (80%)
Negative (%)	9 (64%)	2 (50%)	1 (20%)
Average IEI onset age (range), y	42 (5-66)*	1 (1-2)	7 (1-14)	0.0008‡	0.0016‡	0.4127‡
Average lymphoma onset age (range), y	50 (17-77)	19 (16-20)	11 (2-18)	0.0046‡	0.0003‡	0.0317‡

Values are reported as the n (%) or age (minimal-maximal) of patients unless indicated otherwise.

^*Data are missing for 1 patient in this group.

^†Fisher’s exact test.

^‡Mann-Whitney U test.