Table 1.
Characteristics of the study cohort and the entire population of ALS patients diagnosed during the study period in Stockholm, according to the Swedish Motor Neuron Disease Quality Registry
| Characteristics | Patients of the study cohort | All ALS patients |
|---|---|---|
| (n = 89) | (n = 245) | |
| Age at diagnosis, years | ||
| Mean (SD) | 66.52 (10.69) | 66.16 (11.18) |
| Sex, N (%) | ||
| Male | 54 (60.67%) | 131 (53.47%) |
| Female | 35 (39.33%) | 114 (46.53%) |
| Final diagnosis, N (%) | ||
| ALS | 82 (92.13%) | 218 (88.98%) |
| Other MND | 7 (7.87%) | 27 (11.02%) |
| Site of onset, N (%) | ||
| Bulbar | 38 (42.70%) | 82 (33.88%) |
| Non-bulbar | 51 (57.30%) | 157 (64.88%) |
| Other | — | 3 (1.24%) |
| ALSFRS-R score at diagnosis, mean (SD) | 38.29 (7.85) | 36.84 (8.21) |
| Progression rate at diagnosis, mean (SD) | 0.81 (0.82) | 0.77 (0.70) |
| Diagnostic delay, median | 382 days | 395 days |
| Survival status at the end of follow-up, N (%) | ||
| Dead | 50 (56.18%) | 132 (53.88%) |
| Alive | 39 (43.82%) | 113 (46.12%) |