Fig. 2.

Clinical and biological characteristics of our cohort of sJIA. Mucosal involvement was defined as oral erythema, edema, aphthous ulcers, or ulceration in the nose and throat area. MAS: Macrophage activation syndrome. Green bars show cumulative data during childhood. A patient with known or suspected sJIA was considered as having MAS if Ferritin > 684 ng/ml and 2 of the following criteria were met: Platelet count ≤ 181 × 109/liter, Triglycerides > 156 mg/dl, Fibrinogen ≤ 360 mg/dl, Aspartate aminotransferase > 48 units/liter. Every patient in our cohort had at least 4/5 criteria