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. 2022 Nov 9;9:1028763. doi: 10.3389/fcvm.2022.1028763

TABLE 2.

Baseline characteristics of patients.

Group Value
Age (years)-mean ± SD 47.74 ± 13.85
Female-n (%) 20 (29.4)
BSA (m2)-mean ± SD 1.80 ± 0.19
SCDI (%)-median (IQR) 4.28 (3.67)
Complicating disease-n (%)
 Hypertension 18 (26.5)
 Coronary heart disease 4 (5.9)
 Type 2 diabetes mellitus 4 (5.9)
Gene mutation site-n (%)
 MYH7 16 (23.5)
 MYBPC3 12 (17.6)
 TNNI3 1 (1.5)
 PTPN11 1 (1.5)
 MYBPC3 and MYH7* 1 (1.5)
 Unknown sites 37 (54.4)
NYHA functional class ≥ III-n (%) 18 (26.5)
6-min walk test distance (m)-mean ± SD 451.5 ± 86.0
Symptom-n (%)
 Chest pain 66 (97.1)
 Shortness of breath 54 (79.4)
 Syncope/pre-syncope 31 (45.6)
LVEF (%)-median (IQR) 58 (4)
IVS (mm)-mean ± SD 23.56 ± 4.55
Mitral valve SAM-n (%)
 Grade 0 5 (7.4)
 Grade 1 2 (2.9)
 Grade 2 30 (44.1)
 Grade 3 31 (45.6)
Resting LVOTG (mmHg)-mean ± SD 78 ± 39
Provoked LVOTG (mmHg)-mean ± SD 126 ± 44

*Double mutation; Measured at rest. BSA, body surface area; IQR, interquartile range; IVS, interventricular septum; LVEF, left ventricular ejection fractions; LVOTG, left ventricular outflow tract gradient; NYHA, New York heart association functional class; SAM, systolic anterior motion; SCDI, sudden cardiac death index.