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. 2022 Jul 9;140(12):1335–1344. doi: 10.1182/blood.2022016640

Table 2.

Rate of early ADAMTS13 recovery and relapse

No. of episodes Mean ADAMTS13 recovery slope 95% CI P
Treatment .11
 Rituximab 103 0.9 0.82-0.99
 Corticosteroids alone 13 0.96 0.73-1.19
 Other 12 0.65 0.39-0.90
Race .89
 Black 79 0.88 0.79-0.98
 White 43 0.91 0.76-1.06
 Other/unknown 6 0.96 0.61-1.32
No. of episodes HR (per +0.25 increase in ADAMTS13 recovery slope) 95% CI P
All 128 0.79 0.64-0.98 .03
Rituximab only 103 0.92 0.71-1.18 .5
De novo, rituximab 28 0.58 0.18-1.83 .35
Relapsed, rituximab 75 0.99 0.75-1.31 .94