Table 1.
Demographic characteristics of subjects. Specific ataxia diagnoses are shown in separate lines for each diagnosis represented by more than one subject. Note that mean severity score for Parkinsonism is reported on the UPDRS [40], while ataxia severity scores are on the BARS scale. Ataxia (other) includes: spinocerebellar ataxia type 8, type 14, and type 15; cerebellar-dominant progressive supranuclear palsy; hereditary spastic paraplegia; autoimmune-related ataxia with undefined cause; Behcet’s Disease; autosomal recessive cerebellar ataxia type 1 and type 3; cerebellar hypoplasia; sensory ataxia; Fragile X-Associated Tremor/Ataxia Syndrome; Gordon Holmes’ Syndrome; stroke-related ataxia; sporadic adult-onset ataxia; sporadic adult-onset ataxia with neuropathy; autosomal dominant cerebellar ataxia with unidentified genetic cause.
| n | Age | Women | Men | Severity Score | |
|---|---|---|---|---|---|
| Subjects, Sessions | Mean (SD) | Mean (SD) | |||
| Total | 195, 242 | 46.9 (24.1) | 78 | 117 | n/a |
| Ataxia (all) | 109, 144 | 43.1 (23.8) | 49 | 60 | 10.3 (5.3) |
| AT | 34, 56 | 12.4 (6.1) | 13 | 21 | 11.3 (5.7) |
| Episodic Ataxia | 2, 2 | 50.0 (28.0) | 0 | 2 | 1.2 (0.2) |
| FA | 2, 2 | 55.5 (5.5) | 1 | 1 | 16.2 (2.8) |
| MSA | 5, 6 | 60.4 (5.2) | 2 | 3 | 12.2 (3.8) |
| SCA 1 | 4, 8 | 49.0 (14.1) | 3 | 1 | 8.1 (2.0) |
| SCA 2 | 2, 2 | 61.0 (6.0) | 1 | 1 | 12.0 (1.5) |
| SCA 3 | 11, 14 | 51.0 (10.6) | 9 | 2 | 9.5 (3.3) |
| SCA 6 | 8, 9 | 69.0 (6.0) | 3 | 5 | 12.8 (6.1) |
| SPG 7 | 2, 2 | 58.0 (2.0) | 0 | 2 | 9.0 (1.0) |
| Transient Ataxia | 2, 2 | 72.5 (2.5) | 1 | 1 | 1.0 (0.0) |
| Ataxia (other) | 36, 40 | 55.8 (14.0) | 16 | 20 | 10.6 (5.7) |
| Parkisonism | 52, 59 | 67.6 (7.9) | 14 | 38 | 16.5 (9.7) |
| Control | 34, 39 | 27.5 (18.4) | 15 | 19 | n/a |