. Author manuscript; available in PMC: 2022 Dec 12.

Published in final edited form as: Pediatr Dev Pathol. 2015 Dec 23;18(6):504–511. doi: 10.2350/15-10-1732-OA.1

Table 1.

Malignant Transformation of “CCAM/CPAM 4”

CCAM/CPAM	Ages At Presentation	Follow-up
TYPE 4 ^*	4 cases (13, 18, 26, 28y)	PPB type Ir (2NR, 2LTFU)
	4 cases (1, 1, 2, 2y)	Focal stromal HC (3)
		(INR, 2 LTFU) 1 – “grade 3” PPB at 2y

“TYPE 4 CCAMs show histologic overlap with grade 1 PPBs, and distinction between these entities may not be possible on histology alone.” Adapted from MacSweeney, et al. Am J Surg Pathol 2003; 21:1139–1146.

Abbreviations: y = year; NR = no recurrence; LTFU = lost to follow-up; HC = hypercellularity