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. 2022 Oct 8;210(2):91–103. doi: 10.1093/cei/uxac092

Table 2:

Dosing characteristics, infusion volumes, and infusion flow rates

Children (≥2 to <17 years) Adults (≥17 years) Total
Main study
(n = 38)
Extension
(n = 10)
Main study
(n = 37)
Extension
(n = 17)
Main study
(N = 75)
Extension
(N = 27)
Overall number of infusions (n) 2213 1070 2249 1707 4462 2777
Dose administered (g/kg BW/patient) 0.16 ± 0.05
(0.06–0.29)
0.17 ± 0.08
(0.06–0.30)
0.19 ± 0.07
(0.09–0.39)
0.17 ± 0.07
(0.07–0.38)
0.17 ± 0.07
(0.06–0.39)
0.17 ± 0.08
(0.06–0.38)
Average duration of infusion (active time only) [min] 84.2 ± 45.9
(29.9–230.5)
82.6 ± 28.4
(37.4–126.5)
113.3 ± 48.4
(55.6–304.5)
76.4 ± 39.8
(11.5–130.1)
98.5 ± 49.1
(29.9–304.5)
78.7 ± 35.6
(11.5–130.1)
Infusion volumes and flow rates per patient
 Maximum volume administered (ml) weekly 38.4 ± 20.2
(8.0–90.0)
57.9 ± 29.5
(13.0–102.0)
78.9 ± 31.6
(36.0–159.0)
75.3 ± 38.1
(24.0–150.0)
58.4 ± 33.2
(8.0–159.0)
68.9 ± 35.6
(13.0–150.0)
 Maximum infusion flow rate (ml/h) 39.4 ± 11.1
(15.0–51.8)
42.2 ± 12.9
(20.0–60.0)
60.4 ± 17.5
(29.4–97.9)
91.9 ± 28.3
(45.0–130.9)
49.8 ± 17.9
(15.0–40.0)
73.5 ± 33.9
(20.0–130.9)
 Maximum infusion flow rate/site (ml/h/site) 18.7 ± 6.0
(3.8–30.0)
17.2 ± 4.9
(9.4–25.0)
22.8 ± 9.5
(10.0–51.8)
27.0 ± 8.3
(11.3–43.6)
20.7 ± 8.1
(3.8–51.8)
23.4 ± 8.6
(9.4–43.6)

Data are mean ± SD, (range) except where indicated.

Abbreviations: BW, body weight.