Table 1.

Summary of demographic and clinical information

Categories	Items	Data
Demographic information	Sex	Male: female = 12:20
	Age onset (years, $\overline{\mathrm{x}}\pm \mathrm{s}$)	54.3 $\pm$ 10.2
	Duration of disease (months, $\overline{\mathrm{x}}\pm \mathrm{s}$)	57.8 $\pm$ 51.4
	Family history (%)	9/32 (28.1%)
Clinical presentations	Dementia (%)	27/32 (84.4%)
	Autonomic nervous system dysfunction (%)	22/32 (68.8%)
	Urinary and/or fecal dysfunction (%)	19/32 (59.4%)
	Orthostatic hypotension (%)	3/32 (9.4%)
	Nausea/ vomit (%)	3/32 (9.4%)
	Miosis (%)	2/32 (6.3%)
	Hidrosis (%)	2/32 (6.3%)
	Erectile dysfunction (%)	1/32 (3.1%)
	Episodes of fever (%)	12/32 (37.5%)
	Movement disorder (%)	11/32 (34.4%)
	Parkinsonism (%)	5/32 (15.6%)
	Tremor (%)	6/32 (18.8%)
	Encephalopathy like attacks (%)	11/32 (34.4%)
	Headache (%)	11/32 (34.4%)
	Stroke like attacks (%)	10/32 (31.3%)
	Seizure (%)	4/32 (12.5%)
Examinations	MMSE (0–30, $\overline{\mathrm{x}}\pm \mathrm{s}$)	19.6 $\pm$ 9.2
	MoCA (0–30, $\overline{\mathrm{x}}\pm \mathrm{s}$)	16.7 $\pm$ 8.9
	Abnormal electromyogram (%)	5/12 (41.7%)
	Abnormal electroencephalogram (%)	12/16 (75.0%)
	Abnormal CSF analysis (%)	0/20 (0%)
	CSF Aβ42 (pg/ml, $\overline{\mathrm{x}}\pm \mathrm{s}$)	882.6 $\pm$ 316.3
	CSF t-tau (pg/ml, $\overline{\mathrm{x}}\pm \mathrm{s}$)	172.4 $\pm$ 97.4
	CSF p-tau (pg/ml, $\overline{\mathrm{x}}\pm \mathrm{s}$)	52.2 $\pm$ 22.8
	Abnormal 18F-FDG-PET/CT (%)	2/2 (100%)

Abbreviations: MMSE Mini Mental State Examination, MoCA Montreal Cognitive Assessment, CSF Cerebrospinal fluid