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. 2022 Mar 10;13(5):409–418. doi: 10.1159/000521640

Table 2.

Pathological genes located in the duplicated region of our patient

Gene Disease Inheritance
TBX5 Holt-Oram syndrome AD, haploinsufficiency

TBX3 Ulnar-mammary syndrome AD, LOF

MED13L Transposition of the great arteries, dextro-looped 1 AD, deletion, duplication

Mental retardation and distinctive facial features with or without cardiac defects AD

HSPB8 Neuronopathy, distal hereditary motor, type IIA AD

Charcot-Marie-Tooth disease, axonal, type 2L AD, GOF

CIT Microcephaly 17 AR, LOF

COX6A1 Charcot-Marie-Tooth disease, recessive intermediate D AR, haploinsufficiency

COQ5 Coenzyme Q10 deficiency, primary, 9 AR, GOF

ACADS Deficiency of Acyl-CoA dehydrogenase, short-chain AR, LOF

ORAI1 Immunodeficiency 9 AD, LOF

Myopathy, tubular aggregate, 2 AD, GOF

SETD1B Intellectual developmental disorder with seizures and language delay AD, GOF

GATC Combined oxidative phosphorylation deficiency 42 AR, LOF

HPD Hawkinsinuria, tyrosinemia, type III AR, LOF

CFAP251 Spermatogenic failure 33 AR, deletion

ZCCHC8 Pulmonary fibrosis and/or bone marrow failure, telomere-related, 5 AD, LOF

EIF2B1 Leukoencephalopathy with vanishing white matter; VWM AR

SCARB1 High density lipoprotein cholesterol level QTL6 Variable

DHX37 Neurodevelopmental disorder with brain anomalies and with or without vertebral or cardiac anomalies AR, missense

C12orf65 Combined oxidative phosphorylation deficiency 7 AR, LOF

Spastic paraplegia 55 AR

TCTN2 Meckel syndrome 8 AR

Joubert syndrome 24 AR, LOF

ATP6V0A2 Cutis laxa, autosomal recessive, type IIA AR, LOF

Wrinkly skin syndrome AR, LOF
PUS1 Myopathy, lactic acidosis, and sideroblastic anemia 1 AR, LOF

ANKLE2 Microcephaly 16, primary AR, not known

POLE Susceptibility to colorectal cancer 12 AD

FILS syndrome

IMAGE-I syndrome LOF

HNF1A Type 2 diabetes mellitus; T2D AD

Hepatic adenoma, somatic Renal cell carcinoma, nonpapillary; RCC

Type 1 diabetes mellitus; T1D AR

MODY, type III Diabetes mellitus, insulin-dependent, 20

BCL7A B-cell non-Hodgkin lymphoma, high-grade Not known

DIABLO Deafness, autosomal dominant 64 AD

VPS33A Mucopolysaccharidosis-plus syndrome AR

AD, autosomal dominant; AR, autosomal recessive; LOF, loss of function; GOF, gain of function.