Fig. 2.

Comparison of the reduced/total CoQ₁₀ ratio.

Comparison of the reduced/total CoQ₁₀ ratio in cases with primary CoQ₁₀ deficiency, complex I deficiency, and complex IV or V deficiency. In primary CoQ₁₀ deficiency, the reduced/total CoQ₁₀ ratio was the same as that of the controls. In complex I deficiency, 3/7 cases showed a decreased (< 80% of control value) reduced/total CoQ₁₀ ratio. In complex IV or V deficiency, 3/3 cases showed an increased (120% < of control value) reduced/total CoQ₁₀ ratio. Data are expressed as *P < 0.05, **P < 0.01, and n.s. indicates no significance.