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. 2023 Jan 1;19(2):426–448. doi: 10.7150/ijbs.76223

Table 2.

Mechanism of MQC in ICM

Mitochondrial Quality Control Protein
substrate
Full name Regulators Target cell
Mitochondrial fission Drp1/DLP1 Dynamin-related protein 1 ERK (extracellular regulated protein kinases) Cardiomyocytes/Cardiac microcirculation endothelial cells (CMECs)
Fis1 Fission 1 TBC1D15 (TBC domain family member 15) Cardiomyocytes
Mff Mitochondrial fission factor 1.Voltage-dependent anion channel 1/hexokinase 2 (HK2/VDAC1)
2. DUSP1 (Dual-specificity protein phosphatase1)
Cardiac microcirculation endothelial cells (CMECs)
Mitochondrial fusion OPA1 Optic Atrophy 1 1. TNFα receptor 2 (TNFR2)
2. AMPKα2 (AMP-activated protein kinase)
Cardiomyocytes
Mfn1 Mitofusin1 DNA-dependent protein kinase catalytic subunits (DNA-Pkcs) Cardiomyocytes
Mfn2 Mitofusin2 DNA-dependent protein kinase catalytic subunits (DNA-Pkcs) Cardiomyocytes
Mitophagy
(Receptor-dependent)
FUNDC1 FUN14 domain-containing 1 1. Serine/threonine kinase casein kinase2α (CK2α)
2. Nuclear receptor subfamily 4 group A member 1 (NR4A1)
Cardiomyocytes/Cardiac microcirculation endothelial cells (CMECs)
BNIP3 BCL2/adenovirus E1B 19-kDa interacting protein 3 1. JNK(c-Jun N-terminal kinase)
2. Dual-specificity protein phosphatase1 (DUSP1)
Cardiomyocytes
NIX Nip3-like protein X
Mitophagy
(Receptor-independent)
PINK1/Parkin PTEN induced putative kinase 1 AMP-activated protein kinase-α2 (AMPKα2) Cardiomyocytes/Cardiac microcirculation endothelial cells (CMECs)
Mitochondrial biogenesis (Post-transcriptional regulation) PGC-1 α/PPARγ Peroxisome proliferator activated receptor γ /Peroxisomeproliferator-activated receptor-γ coactivator-1α Cardiomyocytes
NRF1/2 Nuclear respiratory factor 1/2 Cardiomyocytes
Mitochondrial biogenesis (Transcriptional- regulation) TFAM Transcription Factor A, Mitochondrial Cardiomyocytes