Table 3.

Personality evaluation and neuropsychological test performances in ECD patients

	Mean	SD	Reference	t	p
Personality evaluation (BFI, n = 30)
Extraversion	3.10	0.94	3.2	− 0.58	0.56
Agreeableness	4.19	0.49	3.9	3.18	< 0.005*
Conscientiousness	3.77	0.53	3.4	3.81	< 0.001*
Openness	3.40	0.69	3.5	1.61	0.12
Neuroticism	2.72	0.95	3.0	− 0.79	0.44
Neuropsychological test performance (n = 25)
Wisconsin card sorting task
Total number of errors	0.06	1.81	0	0.16	0.88
Non-perseveration errors	− 0.75	1.86	0	− 2.04	0.05
Perseveration errors	− 0.29	2.80	0	− 0.53	0.60
d2 test of attention
KL	96.15	13.25	100	37.01	< 0.0001*
GZ	84.40	20.02	100	16.12	< 0.0001*
GZ-F	86.40	20.79	100	15.99	< 0.0001*
Stroop Test
Word reading	− 0.83	1.48	0	− 2.87	0.024
Color naming	− 0.81	1.72	0	− 2.87	0.008*
Stroop interference	− 0.24	1.31	0	0.92	0.37
California verbal learning test
STFR	− 0.63	1.33	0	− 2.38	0.025
STIR	− 0.84	1.40	0	− 3.01	0.006*
LTFR	− 0.83	1.44	0	− 2.87	0.008*
LTIR	− 1.01	1.39	0	− 3.63	< 0.001*
Verbal fluency tests
Semantic	− 0.48	1.08	0	− 2.29	0.03
Phonetic	− 0.24	1.14	0	− 1.07	0.29
Digit span test
Forward	− 0.47	0.71	0	− 3.36	0.0026*
Backward	− 0.23	0.84	0	− 1.37	0.18
Sequencing	− 0.22	0.86	0	− 1.33	0.20
Trail making test
TMT-A	− 0.63	1.74	0	− 1.86	0.07
TMT-B	− 1.54	4.34	0	− 1.80	0.08

ECD Erdheim-Chester disease, SD standard deviation, BFI Big Five Inventory

*Significant after Bonferroni correction