Table 1.
Case | Age (years) | Sex | Primary Site | Size (cm) | Presentation | Treatment | Status at last follow-up | Follow-up period (months) |
---|---|---|---|---|---|---|---|---|
1 | 67 | Male | Right shoulder infiltrative mass involving soft tissue, bone and lung | 7.8 | Infiltrative shoulder mass | Marginal resection, subsequent wide resection (close margin) of local recurrence, gemcitabine/docetaxel × 3 months-->pazopanib × 2 months-->doxorubicin/olaratumab × 7 cycles-->pebrolizumab--->bevacizumab | DOD (distant lung, spine, pelvic metastases) | 36 |
2 | 63 | Female | Left superoposterior chest wall deep to trapezius muscle | 7.0 | Left shoulder mass with gradual increase in size over 1 year | Radical resection | ANED | 9 |
3 | 75 | Female | Left posterior thigh | 9.1 | Cough and fatigue for 3 months. CT scan reveals lung and mediastinal masses | Radiation to lung, doxil × 3 months, pazopanib | DOD (distant lung, pleural/mediastinal metastases) | 5 |
ANED: alive with no evidence of disease; DOD: dead of disease.