Table 3.

EBV-positive T and NK cell lymphoproliferative disorders

• EBV-positive T/NK lymphoproliferative disorders of childhood*

▪ Hydroa vacciniforme lymphoproliferative disorder*

-Classic

-Systemic

▪ Severe mosquito bite allergy

▪ Chronic active EBV disease, systemic (T and NK cell phenotype)*

▪ Systemic EBV+ T cell lymphoma of childhood

• Extranodal NK/T cell lymphoma, nasal type

• Aggressive NK cell leukemia

• Primary nodal EBV-positive T/NK cell lymphoma*

^*Changes from the 2016 WHO classification

Italics means provisional entity