| ABC | ATP-Binding Cassette |
| ATP | Adenosine Triphosphate |
| CFTR | Cystic fibrosis transmembrane conductance regulator |
| DMEM | Dulbecco’s Modified Eagle’s Medium |
| HEK | Human Embryonic Kidney |
| ICP | intrahepatic cholestasis of pregnancy |
| LPAC | low-phospholipid associated cholelithiasis |
| MSD | Membrane spanning domain |
| NBD | Nucleotide binding domain |
| PC | Phosphatidylcholine |
| PFIC 3 | Progressive familial intrahepatic cholestasis type 3 |
| WT | Wild Type |