Table 1.

Demographics and descriptive statistics of the CF cohort

Variable	n (%)/median (range)
Female sex	24 (32%)
Pancreatic insufficiency	67 (89%)
dF508/dF508, dF508/other, other/other	38 (51%)/34 (45%)/3 (4%)
Age at diagnosis (years)	0.8 (0.0–9.0)
Children treated with CFTR modulators	1 (1%)
Children with CF-related diabetes mellitus	2 (3%)
Chronically infected with Pa during study period	22 (29%)
Age at onset of chronic Pa infection (years)	13.0 (3.1–18.9)
Children with ABPA	3 (4%)
Follow-up time* (years)	9.0 (1.0–14.1)
Number of MBW examinations/child	11 (1–18)
Number of chest CTs/child	3 (1–5)
Chest CTs at MBW examinations (±3 days)	146 (73%)

*Time between the first and the last multiple breath washout or the last chest CT.

ABPA, allergic bronchopulmonary aspergillosis; CFTR, cystic fibrosis transmembrane conductance regulator; MBW, multiple breath washout; Pa, P. aeruginosa.