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. 2023 Jan 27;21:11. doi: 10.1186/s12969-022-00779-3

Table 2.

Clinical features of 39 patients with primary Sjögren’s syndrome diagnosed in childhood

Symptoms & signs N(%)
Glandular enlargement/recurrent parotitis 10 (25.6)
Dry mouth + dry eyes 2 (5.1)
Isolated dry mouth or dry eyes 7 (17.9)
Fever 12 (30.8)
Arthralgia 7 (17.9)
Arthritis 1 (2.6)
Skin involvement 20 (51.3)
Rash 12 (30.8)
Purpura 8 (20.5)
Hematological involvement 14 (35.9)
Leukopenia 7 (17.9)
Thrombocytopenia 6 (15.4)
Anemia 4 (10.3)
Hepatic involvement 13 (33.3)
Lymphadenopathy 9(23.1)
Renal involvement 8 (20.5)
RTA 4 (10.3)
Proteinuria 4 (10.3)
Renal impairment 3 (7.7)
Interstitial pneumonia 3 (7.7)
Neurological involvement 1 (2.6)
Hypokalemia 4 (10.3)
Fatigue 1 (2.6)
Raynaud phenomenon 1 (2.6)