Table 2.
Mean, median, standard deviation of PUMNS, LMNS, MRC values respectively in C9Pos and C9Neg patients
| C9Pos | C9Neg | SD | P valuea | ||||
|---|---|---|---|---|---|---|---|
| Mean | Median | SD | Mean | Median | |||
| PUMNS | 129 | 12.5 | 7.6 | 10.0 | 9.0 | 7.3 | 0.010 |
| Bulbar | 1.9 | 2.0 | 1.3 | 1.4 | 1.0 | 1.2 | 0.005 |
| Upper limbs | 5.4 | 4.5 | 3.7 | 4.2 | 4.0 | 3.8 | 0.027 |
| Lower limbs | 5.7 | 6.0 | 3.6 | 4.5 | 4.0 | 3.6 | 0.023 |
| LMNS | 5.2 | 4.0 | 4.0 | 5.2 | 5.0 | 3.4 | ns |
| Upper limbs | 2.0 | 2.0 | 2.0 | 2.5 | 2.0 | 1.9 | ns |
| Lower limbs | 2.4 | 2.0 | 2.2 | 2.0 | 2.0 | 1.9 | ns |
| MRC | 49.0 | 52.0 | 10.0 | 49.1 | 52.0 | 10.3 | ns |
| Upper limbs | 25.2 | 26.0 | 5.3 | 24.0 | 26.0 | 6.2 | ns |
| Lower limbs | 23.8 | 26.0 | 6.5 | 25.2 | 28.0 | 6.3 | ns |
ns, not significant; C9Pos, patients carrying C9orf72 repeat expansion; C9Neg, patients without C9orf72 repeat expansion; PUMNS, Penn Upper Motor Neuron Score; LMNS, Lower Motor Neuron Score; MRC, Medical Research Council; SD, standard deviation
aComparison between C9Pos and C9Neg patients