Table 3. European Incidence Rate of FTLD Phenotype Cases per 100 000 Person-Years^a.

Phenotype	Total		Rate (95% CI), cases per 100 000 person-years		Random-intercept variance, sex-adjusted model
	Rate (95% CI), cases per 100 000 person-years	Random-intercept variance	Male	Female
BVFTD	0.83 (0.52-1.32)	0.48	0.99 (0.60-1.62)	0.67 (0.40-1.13)	0.48
PPA	0.61 (0.42-0.88)	0.15	0.74 (0.49-1.12)	0.48 (0.31-0.76)	0.15
CBS or PSP	0.51 (0.22-1.20)	1.94	0.59 (0.25-1.41)	0.44 (0.18-1.06)	1.93
FTD-ALS	0.11 (0.05-0.26)	0.81	0.16 (0.06-0.39)	0.08 (0.03-0.23)	0.80

Abbreviations: BVFTD, behavioral variant frontotemporal dementia; CBS, corticobasal syndrome; FTD-ALS, frontotemporal dementia with amyotrophic lateral sclerosis; FTLD, frontotemporal lobar degeneration; PPA, primary progressive aphasia; PSP, progressive supranuclear palsy.

^a Estimates of incidence and sex-specific incidence are derived from random-intercept Poisson models. The estimated variance of the random intercept (measure of incidence heterogeneity across registries) is also reported.