Skip to main content
. Author manuscript; available in PMC: 2023 Apr 29.
Published in final edited form as: Circ Res. 2022 Apr 28;130(9):1365–1381. doi: 10.1161/CIRCRESAHA.122.320084

Table 1:

Classification of Pulmonary Hypertension (From 2)

1. Pulmonary Arterial Hypertension (PAH)
  • 1.1

    Idiopathic PAH

  • 1.2

    Heritable PAH

  • 1.3

    Drug- and toxin-induced PAH

  • 1.4
    PAH associated with:
    • 1.4.1
      Connective tissue disease
    • 1.4.2
      HIV infection
    • 1.4.3
      Portal hypertension
    • 1.4.4
      Congenital heart disease
    • 1.4.5
      chistosomiasis
  • 1.5

    PAH long-term responders to calcium blockers

  • 1.6

    PAH with overt features of venous/capillaries involvement

  • 1.7

    Persistent pulmonary hypertension (PH) of the newborn syndrome
2. PH due to left heart disease
3. PH due to lung diseases and/or hypoxia
4. PH due to pulmonary artery obstructions
5. PH with unclear and/or multifactorial mechanisms