TABLE 3.
Mortality in ARM affected births from programs contributing to the study for all years available in each program, ICBDSR
| Country- program | Surveillance period | Number of live births with ARM | Live birth prevalence per 10,000 births (95% CI) | Age at deatha |
||||||
|---|---|---|---|---|---|---|---|---|---|---|
| Day 1 |
Day 2–6 |
Day 7–27 |
Day 28- Month 12 |
Year 1–4 |
Year 5 and above |
Death time unknown |
||||
| n (%) | n (%) | n (%) | n (%) | n (%) | n (%) | n (%) | ||||
| Argentina-RENAC | 2009–2014 | 486 | 4.75 (4.34, 5.19) | 145 (29.8) | − | − | − | − | − | |
| Colombia-Bogotá | 2001–2014 | 39 | 0.96 (0.68, 1.31) | 1 (2.6) | − | − | − | − | − | − |
| Colombia-Cali | 2011–2014 | 2 | 0.73 (0.07, 2.67) | − | − | − | − | − | − | − |
| Czech Republic | 1994–2014 | 766 | 3.57 (3.32, 3.83) | 12 (1.6) | 15 (2.0) | 13 (1.7) | 30 (3.9) | 2 (0.3) | 7 (0.9) | − |
| France-Paris | 1981–2014 | 183 | 2.09 (1.80, 2.42) | 8 (4.4) | 7 (3.8) | 6 (3.3) | − | − | − | 0 (0) |
| Germany-Saxony Anhalt | 1980–2014 | 170 | 3.23 (2.76, 3.75) | 3 (1.8) | 5 (2.9) | 2 (1.2) | 7 (4.1) | 2 (1.2) | 0 (0) | 0 (0) |
| Iran-TROCA | 2005–2012 | 131 | 9.24 (7.73, 10.96) | 0 (0) | 0 (0) | − | − | − | − | − |
| Israel-SMCb | 2000–2014 | 53 | 2.64 (1.98, 3.45) | 0 (0) | 0 (0) | 2 (3.8) | 2 (3.8) | − | − | − |
| Italy-Lombardy | 2003–2012 | 46 | 3.45 (2.53, 4.61) | 0 (0) | 0 (0) | 1 (2.2) | 3 (6.5) | 1 (2.2) | 0 (0) | 0 (0) |
| Italy-Tuscany | 1992–2014 | 117 | 1.83 (1.52, 2.20) | 2 (1.7) | 3 (2.6) | 0 (0) | 2 (1.7) | 1 (0.9) | 0 (0) | 0 (0) |
| Malta-MCAR | 1995–2013 | 27 | 3.38 (2.23, 4.91) | 0 (0) | 0 (0) | 1 (3.7) | 0 (0) | 0 (0) | 0 (0) | − |
| Mexico- Nuevo Leon | 2011–2015 | 19 | 0.43 (0.26, 0.67) | 0 (0) | 2 (10.5) | 1 (5.3) | 1 (5.3) | |||
| Mexico- RYVEMCE | 1978–2013 | 471 | 3.93 (3.58, 4.30) | 85 (18.0) | 22 (4.7) | − | − | − | − | 2 (0.4) |
| Netherlands-Northern | 1981–2014 | 187 | 3.32 (2.87, 3.84) | 13 (7.0) | 19 (10.2) | 3 (1.6) | 7 (3.7) | 1 (0.5) | 0 (0) | 0 (0) |
| Slovak Republic | 2001–2014 | 262 | 3.37 (2.97, 3.80) | 0 (0) | 23 (8.8) | 6 (2.3) | − | − | − | − |
| South America | 1995–2014 | 1,479 | 5.05 (4.80, 5.32) | 344 (23.3) | 72 (4.9) | 43 (2.9) | 5 (0.3) | − | − | 20 (1.4) |
| Spain-ECEMC | 1980–2013 | 554 | 1.92 (1.76, 2.08) | 55 (9.9) | 9 (1.6) | − | − | − | − | − |
| Sweden | 1974–2014 | 1,228 | 2.93 (2.77, 3.10) | 31 (2.5) | 42 (3.4) | 22 (1.8) | 28 (2.3) | 15 (1.2) | 7 (0.6) | 0 (0) |
| Ukraine-OMNI-Net | 2000–2013 | 88 | 2.18 (1.75, 2.68) | 2 (2.3) | 2 (2.3) | 6 (6.8) | 13 (14.8) | 1 (1.1) | 0 (0) | 2 (2.3) |
| United Kingdom-Wales | 1998–2014 | 172 | 3.02 (2.59, 3.51) | 6 (3.5) | 7 (4.1) | 3 (1.7) | 4 (2.3) | 0 (0) | 0 (0) | |
| USA-Arkansas | 1993–2012 | 329 | 4.32 (3.87, 4.82) | 15 (4.6) | 11 (3.3) | 4 (1.2) | 10 (3.0) | 3 (0.9) | 3 (0.9) | 0 (0) |
| USA-Atlanta | 1974–2008 | 485 | 3.60 (3.28, 3.93) | 60 (12.4) | 20 (4.1) | 8 (1.6) | 17 (3.5) | 0 (0) | 3 (0.6) | 1 (0.2) |
| USA-Texas | 1996–2012 | 1,068 | 1.79 (1.68, 1.90) | 3 (0.3) | 7 (0.7) | 13(1.2) | 55 (5.1) | 16 (1.5) | 5 (0.5) | 0 (0) |
| USA-Utah | 1999–2012 | 221 | 3.07 (2.68, 3.51) | 14 (6.3) | 7 (3.2) | 3 (1.4) | 20 (9.0) | 4 (1.8) | 2 (0.9) | 0(0) |
| TOTAL | 1974–2014 | 8,583 | 2.96 (2.90, 3.03) | 654 (7.6c) | 418 (4.9c,d) | 137 (2.0c) | 197 (3.1c) | 46 (0.9c) | 27 (0.6c) | 26 (0.4c) |
Abbreviations: ECEMC, Registry of the Spanish Collaborative Study of Congenital Malformations; ECLAMC, Latin American Collaborative Study of Congenital Malformations; ETOPFA, Elective Termination of Pregnancy for Fetal Anomalies; MCAR, Malta Congenital Anomalies Registry; OMNI-Net, Ukraine Birth Defects Prevention Program; RENAC, National Network of Congenital Anomalies of Argentina; RYVEMCE, Mexican Registry and Epidemiological Surveillance of External Congenital Malformations; SMC, Soroka Medical Center; TROCA, Tabriz Registry of Congenital Anomalies; USA, United States of America.
A hyphen (–) means that the registry did not report follow-up data for that time period.
Data on livebom children with anorectal atresia from one hospital.
Excludes programs that have no data on mortality for selected age at death.
Frequency and percentage refer to first week mortality.