Table 1.
Demographic characteristics of the 52 cases of anti-p200 pemphigoid with mucosal lesions.
| Items | Mean of ages (SD) | Number of cases (Percentage) |
|---|---|---|
| Gender | ||
| Male | 63.7 (16.0) | 30 (57.7%) |
| Female | 58.7 (21.8) | 19 (36.5%) |
| Unknown | Unknown | 3 (5.8%) |
| Geographical distribution of reported cases | ||
| Germany | 56.1 (21.7) | 14 (26.9%) |
| France | 75.1 (12.3) | 11 (21.2%) |
| Japan | 59.5 (16.8) | 10 (19.2%) |
| India | 58.2 (22.5) | 9 (17.3%) |
| USA | 65.7 (15.3) | 3 (5.8%) |
| China | 55.7 (7.0) | 3 (5.8%) |
| Korea | 49 (/) | 1 (1.9%) |
| Poland | 52 (/) | 1 (1.9%) |
| Final diagnosis | ||
| Anti-p200 pemphigoid | 60.9 (20.1) | 38 (73.1%) |
| Anti-p200 pemphigoid + anti-LM332-type MMP | 63.2 (5.8) | 8 (15.4%) |
| Anti-p200 pemphigoid + EBA | 58.5 (9.2) | 2 (3.8%) |
| Anti-p200 pemphigoid + anti-BP180-type MMP | 87 (/) | 1 (1.9%) |
| Anti-p200 pemphigoid + BP | 68 (/) | 1 (1.9%) |
| Anti-p200 pemphigoid + BP + anti-LM332-type MMP + anti-CNTN1-positive IP | 77 (/) | 1 (1.9%) |
| Anti-p200 MMP | 49 (/) | 1 (1.9%) |
LM332, laminin 332; MMP, mucous membrane pemphigoid; BP, bullous pemphigoid; EBA, epidermolysis bullosa acquisita; anti-CNTN1-positive IP, anti-contactin-1-positive inflammatory polyneuropathy; “/”, not applicable.