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. 2023 Feb 13;10:1108623. doi: 10.3389/fmed.2023.1108623

Table 2.

Differential diagnosis of morphea types.

Morphea type Differential diagnoses
Limited morphea
Early stage Lichen sclerosus
Granuloma annulare
Cutaneous mastocytosis
Erythema cronicum migrans
Porokeratosis Mibelli
Mycosis fungoides
Vitiligo
Annular lichenoid dermatitis of youth (ALDY)
Late stage
prevalent atrophy
prevalent sclerosis
prevalent hyperpigmentation
Lichen sclerosus
Morpheaform injection-site reactions
Scarring
Acrodermatitis chronica atrophicans
Lipodermatosclerosis
Carcinoma en cuirasse
Sclerosing congenital melanocytic nevus/ connective tissue nevi
Morpheaform basal cell carcinoma
Necrobiosis lipoidica
Pretibial myxedema
Postinflammatory hyperpigmentation
Erythema discromicum perstans
Cafe-au-lait spots
Generalized morphea
Systemic sclerosis (scleroderma)
Scleredema
Scleromyxedema
Chronic graft-versus-host disease
Porphyria cutanea tarda
Primary systemic amyloidosis
Nephrogenic systemic fibrosis
Morpheaform sarcoidosis
Paraneoplastic scleroderma-like syndromes (e.g., POEMS syndrome)
Phenylketonuria
Genetic disorders
Linear morphea
Panniculitis
Localized lipodystrophy
Steroid-induced atrophy
Sclerosing nevus
Lupus erythematosus profundus
Focal dermal hypoplasia
Reflex sympathetic dystrophy
Diabetic cheiroartropathy
Eosinophilic fasciitis
Deep morphea
Panniculitis Scleredema Lipodystrophy Eosinophilic fasciitis