Table 1.

American Thoracic Society/European Respiratory Society Classification of Idiopathic Interstitial Pneumonias Based on Multidisciplinary Diagnoses

Major idiopathic interstitial pneumonia   Idiopathic pulmonary fibrosis (IPF)   Idiopathic nonspecific interstitial pneumonia (NSIP)   Respiratory bronchiolitis-interstitial lung disease (RB-ILD)   Desquamative interstitial pneumonia (DIP)   Cryptogenic organizing pneumonia (COP)   Acute interstitial pneumonia (AIP)

Rare idiopathic interstitial pneumonias  Idiopathic lymphoid interstitial pneumonia (LIP)  Idiopathic pleuroparenchymal fibroelastosis

Unclassifiable idiopathic interstitial pneumonia

Table adapted from Travis, W.D., Costabel, U., Hansell, D.M., King, T.E., Lynch, D.A., Nicholson, A.G., Ryerson, C.J., Ryu, J.H., Selman, M., Wells, A.U., Behr, J., Bouros, D., Brown, K.K., Colby, T. V., Collard, H.R., Cordeiro, C.R., Cottin, V., Crestani, B., Drent, M., Dudden, R.F., Egan, J., Flaherty, K., Hogaboam, C., Inoue, Y., Johkoh, T., Kim, D.S., Kitaichi, M., Loyd, J., Martinez, F.J., Myers, J., Protzko, S., Raghu, G., Richeldi, L., Sverzellati, N., Swigris, J., Valeyre, D., 2013. An official American Thoracic Society/European Respiratory Society statement: Update of the international multidisciplinary classification of the idiopathic interstitial pneumonias. Am. J. Respir. Crit. Care Med. 188, 733–748.