Supplementary material for Lee et al., Proc. Natl. Acad. Sci. USA, 10.1073/pnas.140082197
Table 5.
Nitrogen kinetics in OTC carriers receiving 0.4 g protein/kg per daySubject | Diagnosis | Urea flux, µmol/kg per h | Glutamine flux, µmol/kg per h | 15 N-urea/15N-glutamine |
Symptomatic | ||||
1001 | OTCF | 115 | 491 | 0.174 |
1002 | OTCF | 102 | 394 | 0.188 |
Mean |
| 108 | 442 | 0.18 |
SD |
| 9 | 68 | 0.01 |
Asymptomatic | ||||
1003 | OTCF | 132 | 267 | 0.218 |
1004 | OTCF | 66 | 313 | 0.299 |
1005 | OTCF | 145 | 470 | 0.216 |
1006 | OTCF | 99 | 259 | 0.211 |
1007 | OTCF | 73 | 455 | 0.262 |
1008 | OTCF | 92 | 458 | 0.241 |
1009 | OTCF | 92 | 383 | 0.273 |
1010 | OTCF | 96 | 442 | 0.349 |
Mean |
| 99 | 380 | 0.26 |
SD |
| 27 | 89 | 0.04 |
OTCF, OTC-deficient female.