Table 1.
Values for serum C4, C1inhA and C1inhF in control individuals and hereditary angio-oedema (HAE) patients.
| Control | HAE (untreated) | HAE (treated) | |
|---|---|---|---|
| C4 (g/l) (median, range), normal range 0.14–0.54 g/l | 0.22 (0.09–0.36) | 0.06 (0.01–0.23) | 0.10 (0.01–0.29) |
| C1inhA (mg/l) (mean, s.d.), normal range 150–350 mg/l | 302 (72) | 58 (32) | 74 (31) |
| C1inhF (%) (mean, SD), normal range > 84% | 106 (8) | 58 (25) | 71 (22) |