Ependymomas are frequently diagnosed in NF2 patients and may occur in a
variety of locations including unusual sites. Post-gadolinium T1-weighted
magnetic resonance imaging of an NF2 patient shows a weakly enhancing
intraventricular mass in the fourth ventricle (a). A second NF2 patient
developed an intramedullary mass in the cervical spine (b). Histologically, the
fourth ventricular mass exhibited typical features of ependymoma including
prominent perivascular pseudorosettes and scattered true ependymal rosettes (c,
d), with some regions exhibiting prominent papillary architecture (e). Scale
bars 100 μm (c), 20 μm (d), 50 μm (e).