Table 1.
Patient demographics and characteristics (deceased CD and matched-control CD cohorts).
Patient ID | Diagnosis | Histopathology | Sex | Age at diagnosis | |
---|---|---|---|---|---|
Deceased CD group | 1 | UCD | Hyaline vascular | Male | 13·5 |
2 | iMCD | Hypervascular | Female | 15·2 | |
3 | iMCD | Hypervascular | Male | 17·0 | |
4 | iMCD | NS | Female | 43·4 | |
5 | iMCD | Hypervascular | Female | 65·5 | |
6 | iMCD | Hypervascular | Female | 61·3 | |
7 | iMCD | Mixed | Male | 66·7 | |
8 | POEMS-associated MCD | Plasmacytic | Male | 52·3 | |
9 | POEMS-associated MCD | NS | Male | 40·5 | |
10 | HHV8-associated MCD | Plasmablastic | Female | 80·8 | |
Matched-control CD cohort | 11 | UCD | Mixed | Male | 48·5 |
12 | UCD | NS | Female | 19·0 | |
13 | iMCD | Hypervascular | Male | 13·9 | |
14 | iMCD | Hypervascular | Female | 21·7 | |
15 | iMCD | Hypervascular | Female | 18·5 | |
16 | iMCD | Hypervascular | Male | 2·6 | |
17 | iMCD | Mixed | Female | 45·7 | |
18 | iMCD | Hypervascular | Female | 39·8 | |
19 | iMCD | Hypervascular | Female | 65·9 | |
20 | iMCD | Mixed | Male | 47·6 | |
21 | iMCD | Hypervascular | Male | 65·2 | |
22 | iMCD | Hypervascular | Female | 40·3 | |
23 | iMCD | Plasmacytic | Female | 53·7 | |
24 | iMCD | Mixed | Female | 50·7 | |
25 | POEMS-associated MCD | Mixed | Male | 43·0 | |
26 | POEMS-associated MCD | Mixed | Male | 39·7 | |
27 | POEMS-associated MCD | NS | Male | 56·7 | |
28 | HHV8-associated MCD | Plasmablastic | Male | 68·1 | |
29 | HHV8-associated MCD | Plasmablastic | Female | 64·2 |
CD, Castleman disease; HHV8, human herpesvirus 8; iMCD, idiopathic multicentric Castleman disease; NS, not stated; POEMS, polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy and skin changes; UCD, unicentric Castleman disease.