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. Author manuscript; available in PMC: 2014 Jul 1.
Published in final edited form as: Medicine (Baltimore). 2013 Jul;92(4):223–243. doi: 10.1097/MD.0b013e31829d08f9

Table 15.

Proposed new classification of juvenile idiopathic inflammatory myopathies

Clinical Phenotype

Dermatomyositis (JDM)
Polymyositis (JPM)
Overlap myositis (JCTM)
Malignancy-associated myositis
Inclusion body myositis

Autoantibody Phenotype

Myositis-specific autoantibodies (MSA)
 Anti-synthetases (including anti-Jo-1)
 Anti-signal recognition particle
 Anti-Mi-2
 Anti-p155/140
 Anti-MJ
Myositis-associated autoantibodies (MAA)
MSA/MAA negative