Table 15.
Proposed new classification of juvenile idiopathic inflammatory myopathies
Clinical Phenotype |
|
Dermatomyositis (JDM) |
Polymyositis (JPM) |
Overlap myositis (JCTM) |
Malignancy-associated myositis |
Inclusion body myositis |
|
Autoantibody Phenotype |
|
Myositis-specific autoantibodies (MSA) |
Anti-synthetases (including anti-Jo-1) |
Anti-signal recognition particle |
Anti-Mi-2 |
Anti-p155/140 |
Anti-MJ |
Myositis-associated autoantibodies (MAA) |
MSA/MAA negative |