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. Author manuscript; available in PMC: 2019 Mar 1.
Published in final edited form as: J Pediatr. 2017 Dec 1;194:158–164.e1. doi: 10.1016/j.jpeds.2017.10.026

Table 4. Histology from Autopsies of Infants with Classic Presentation of ACDMPV.

Histologic assessment focused on areas of congested, non-collapsed lung, in which architecture and capillaries were well visualized.

Infant 1 2 3
Age at Presentation Birth Birth 1 day
Age at Death 15 days 9 days 8 days
Deficient capillarization of alveoli Extensive Extensive Extensive
Malposition of pulmonary veins Extensive Extensive Extensive
Medial hypertrophy of small arteries and arterioles Mild Mild Mild
Lobular maldevelopment Definite Definite Definite
Lymphangiectasis Diffuse, interlobular Diffuse, interlobular Diffuse, interlobular