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. 1987 Feb;46(2):153–155. doi: 10.1136/ard.46.2.153

SLE-like and sicca symptoms in late component (C9) complement deficiency.

M Sugimoto, M Nishikai, A Sato, Y Suzuki, M Nihei, J Uchida, N Mimura
PMCID: PMC1002082  PMID: 3827337

Abstract

Hereditary deficiencies in early and late complement components are well known to predispose to SLE-like syndromes or recurrent infection. Hitherto reported C9 deficient cases have usually been healthy subjects, however, and it is not considered that C9 deficiency is associated with any specific disease. We describe a completely C9 deficient patient with possible Sjögren's syndrome and discuss the relationship.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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