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. 1988 Mar;47(3):218–223. doi: 10.1136/ard.47.3.218

The arthropathy of cystic fibrosis.

J Dixey 1, A N Redington 1, R C Butler 1, M J Smith 1, J R Batchelor 1, D F Woodrow 1, M E Hodson 1, J C Batten 1, D A Brewerton 1
PMCID: PMC1003487  PMID: 3355258

Abstract

Musculoskeletal symptoms are frequent in cystic fibrosis (CF). Here the clinical features of 29 patients with CF who had significant arthropathy are described. Twelve had episodic arthritis (EA) characterised by repeated short attacks of severe, incapacitating polyarthritis, which in seven was associated with fever and erythema nodosum. Ten patients had hypertrophic pulmonary osteoarthropathy (HPOA). The onset of symptoms in the group with HPOA was usually later (mean age 20 years v 16 years for EA) and was associated with significantly worse lung function than in patients with CF, either without arthropathy or with EA. Seven patients had arthropathies which could not be classified as EA or HPOA.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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