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. 1990 May;63(5):308–310. doi: 10.1136/hrt.63.5.308

Sudden death in hypertrophic cardiomyopathy with normal left ventricular mass.

B J Maron 1, A H Kragel 1, W C Roberts 1
PMCID: PMC1024484  PMID: 2278803

Abstract

An active, healthy, and symptom free 16 year old boy with a family history of hypertrophic cardiomyopathy died suddenly while walking home from school. Necropsy showed absence of left ventricular hypertrophy (that is, normal heart weight), though the characteristic histological abnormalities of hypertrophic cardiomyopathy, such as cardiac muscle cell disorganisation and abnormal intramural coronary arteries, were present. It is likely that this patient had hypertrophic cardiomyopathy and died before left ventricular hypertrophy developed.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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